Successful Pregnancy Outcome by Caesarean Section in a Woman with Arthrogryposis Multiple Congenita (AMC)
), Anshu Paul(2), Smiti Nanda(3), Suresh Kumar Singhal(4),
(1)
(2)
(3)
(4)
Corresponding Author
Abstract
Arthrogryposis Multiplex Congenita (AMC) is a symptom complex of congenital joint contractures associated with neurogenic and myopathic disorders. It is diagnosed at birth and often progresses to a state of significant disability. Pregnancy in a woman with AMC is at high risk due to diminished pulmonary reserve, increased risk of thromboembolism and anesthesia. Successful pregnancy in patients with AMC is very rare and only five cases have been reported in literature. Present case is being reported due to its rarity (Afr. J. Reprod. Health 2010; 14[3]: 233-234).
Résumé
L’arthrogrypose congénitale multiple (ACM) est un symptôme complexe des contractures articulaires congénitales liées aux troubles neurogènes et myopathiques. Il est diagnostiqué à la naissance et progresse souvent jusqu’à un état d’incapacité significative. La grossesse chez une femme qui souffre de l’ACM est à haut risque dû au réserve pulmonaire réduit, un risque élevé de la thromboembolie et de l’anesthésie. La grossesse réussite chez les patientes atteintes de l’ACM est très rare et il n’y a que cinq cas qui ont été signalés dans la littérature. Ce cas présent est signalé à cause de sa rareté (Afr. J. Reprod. Health 2010; 14[3]: 233-234).
Key words: Arthrogryposis multiplex congenita, pregnancy, successful outcome.
References
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